Asunto(s)
Persona de Mediana Edad , Femenino , Humanos , Carcinoma de Células Escamosas/secundario , Neoplasias de los Músculos/secundario , Neoplasias Pulmonares/patología , Carcinoma de Células Escamosas , Resultado Fatal , Espectroscopía de Resonancia Magnética , Neoplasias de los Músculos , Neoplasias PulmonaresAsunto(s)
Persona de Mediana Edad , Femenino , Humanos , Carcinoma de Células Escamosas/secundario , Neoplasias Pulmonares/patología , Neoplasias de los Músculos/secundario , Carcinoma de Células Escamosas/diagnóstico por imagen , Resultado Fatal , Neoplasias Pulmonares/diagnóstico por imagen , Espectroscopía de Resonancia Magnética , Neoplasias de los Músculos/diagnóstico por imagenAsunto(s)
Persona de Mediana Edad , Femenino , Humanos , Carcinoma de Células Escamosas/secundario , Neoplasias Pulmonares/patología , Neoplasias de los Músculos/secundario , Carcinoma de Células Escamosas/diagnóstico por imagen , Resultado Fatal , Neoplasias Pulmonares/diagnóstico por imagen , Espectroscopía de Resonancia Magnética , Neoplasias de los Músculos/diagnóstico por imagenRESUMEN
Catastrophic antiphospholipid syndrome (CAPS) is an acutely devastating situation characterized by widespread thrombotic microangiopathy in the presence of elevated titers of antiphospholipid antibodies. We describe a 57-year old woman who underwent liver transplantation for primary sclerosing cholangitis and developed this malignant variant of the antiphospholipid syndrome.
Asunto(s)
Síndrome Antifosfolípido/etiología , Trasplante de Hígado/efectos adversos , Complicaciones Posoperatorias , Colangitis Esclerosante/cirugía , Femenino , Humanos , Persona de Mediana EdadRESUMEN
We describe a 26-year-old white female with a history of Raynaud phenomenon, erythema nodosum, polyarthralgias, migraine, vertigo, seizures, transient ischemic attacks, one fetal loss, and false positive VDRL, who developed milk hypertension without overt lupus nephritis. She had positive antinuclear antibodies (ANA) and double-stranded deoxyribonucleic acid (dsDNA) antibodies. The lupus anticoagulant test (LAC) and cardiolipins antibodies (aCL) were positive. She was diagnosed as having a Systemic Lupus Erythematosus-like illness (SLE-like) with 'secondary' antiphospholipid syndrome (APS). Renal spiral computed tomography (CT) with intravenous (IV) contrast showed bilateral renal artery stenosis. Anticoagulation with acenocumarol was started. She became normotensive without antihypertensive drugs five months later. A follow-up renal spiral CT showed complete recanalization of both renal arteries, making thrombosis the more likely culprit pathology in the stenosis. After two years follow up the patient is normotensive. She remains on acenocumarol.